Dietary Management of Hereditary Fructose Intolerance

Tip 1 - Hereditary fructose intolerance

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Tip 2 - Hereditary fructose intolerance.

Hereditary fructose intolerance (HFI, OMIM 22960), caused by catalytic deficiency of aldolase B (fructose-1,6-bisphosphate aldolase, EC 4.1.2.13), is a recessively inherited condition in which affected homozygotes develop hypoglycaemic and severe abdominal ...